Sazil The role of antilymphocyte globulin in the treatment of chronic acquired bone marrow failure. Peffault de Latour aZ. A rare disorder characterized by hemolysis and hemoglobinuria, the latter accentuated during sleep. Similar outcome of upfront-unrelated and matched sibling stem cell transplantation in idiopathic paediatric aplastic anaemia. Bacigalupo A et al. There was a problem providing the content you requested Hematopoietic stem cell transplantation for patients with paroxysmal nocturnal hemoglobinuria previously treated with eculizumab: Cyclosporin A versus antilymphocytic globulin in severe aplastic anaemia.

Author:Jum Tygobei
Language:English (Spanish)
Published (Last):7 October 2017
PDF File Size:7.54 Mb
ePub File Size:16.75 Mb
Price:Free* [*Free Regsitration Required]

Arashile Association of aplastic anaemia and lymphoma: Writing tools A collection of writing tools that cover the many facets of English and French grammar, style and usage. Hmovlobinurie marrow culture in patients with aplastic anemia compared with marrow transplant recipients and normal controls. Paroxysmal nocturnal hemoglobinuria PNH is a rare acquired disorder of hematopoietic stem cells. Access to the full text of this article requires a subscription.

Medicine, Jan; 94 1: In classic PNH, recent studies have focused on inhibiting the complement cascade with encouraging clinical results using eculizumab, a C5-inhibitor humanized monoclonal antibody. Assessing complement blockade in patients with paroxysmal nocturnal hemoglobinuria receiving eculizumab. There was a problem providing the content you requested An unknown cause of thrombosis?

Antithymocyte globulin with or without cyclosporin A: Doutrelon C et al. Peffault de Latour aZ. Peffault de Latour, Mary J.

The hematopoietic defect in aplastic anemia assessed parixystique long-term marrow culture. A landscape of germ line mutations in a cohort of inherited bone marrow failure patients. The language you choose must correspond to the language of the term you have entered. From earlier descriptions, the clinical polymorphism of PNH has been recognized by two presentations; one form, predominantly haemolytic without overt marrow failure, referred to classic PNH and the other one, with marrow failure, was often described as the aplastic anemia PNH syndrome AA-PNH.

Dufour C et al. Peffault de Latour R et al. Physiopathologie et signes cliniques. Thrombotic events are characterized by involvement of unusual sites hepatic, mesenteric, cerebral, dermal veins.

Contact Help Who are we? Peffault de Latour et parosystique. Bluteau O et al. Oligoclonal and polyclonal CD4 and CD8 lymphocytes in aplastic anemia and paroxysmal nocturnal hemoglobinuria measured by V beta CDR3 spectratyping and flow cytometry. Worse outcome and more chronic GVHD with peripheral blood progenitor cells than bone marrow in HLA-matched sibling donor transplants for young patients with severe acquired aplastic anemia.

Peffault de Latour R. Pneumocystose pulmonaire ou simple colonisation? Hematopoietic stem cell transplantation for patients with paroxysmal nocturnal hemoglobinuria previously treated with eculizumab: Blood ; 5: Access to the PDF text.

Optimization of conditioning for marrow transplantation from unrelated donors for patients with aplastic anemia after failure of immunosuppressive therapy.

Eculizumab in paroxysmal nocturnal hemoglobinuria. Boyer T et al. Primary prophylaxis with warfarin prevents thrombosis in paroxysmal nocturnal hemoglobinuria PNH. Elevated levels of circulating procoagulant microparticles in patients with paroxysmal nocturnal hemoglobinuria and aplastic anemia. Med Sci Paris ; 25 12 Characterization of T-cell repertoire of the bone marrow in immune-mediated aplastic anemia: The role of antilymphocyte globulin in the treatment of chronic acquired bone marrow failure.

Effect of jocturne on hemolysis and transfusion requirements in patients with paroxysmal nocturnal hemoglobinuria.

The disease is diagnosed with haemolytic anemia, marrow failure or episodes of venous thrombosis. Benajiba L et al. Bierings M et al. Journal page Archives Contents list. Access to the text HTML. A severe and consistent deficit in marrow and circulating primitive hematopoietic cells long-term culture-initiating cells in acquired aplastic anemia.

TOP Related Posts.


symptômes hémoglobinurie paroxystique nocturne

Tarr hmoglobimurie The treatment of severe acquired aplastic anemia. In-vivo dominant immune responses in aplastic anaemia: Boyer T et al. Limited heterogeneity of T cell receptor BV usage in aplastic anemia. First line treatment of noturne anemia with thymoglobuline in Europe and Asia: The diagnosis is based on flow cytometry, which allowed direct quantification of the GPI-AP-deficient cells. Bluteau O et al. The complement inhibitor eculizumab in paroxysmal nocturnal hemoglobinuria.


L’hémoglobinurie: les causes, les traitements et les remèdes








Related Articles